Wolf-Hirschhorn Syndrome (4p- Syndrome)

CNS

• Mental/motor retardation
• Hypotonia
• Seizures

Airway

• Micrognathia
• Cleft lip/teeth
• Funky dentition

Respiratory

Respiratory embarassment Aspiration

CV

• ASD
• VSD

Musculoskeletal

• scoliosis

Considerations

• Airway challenge
• Seizure medications may affect drug metabolism
• SBE prophylaxis for CHD