Aase-Smith Syndrome

General

• Joint abnormalities

Airway

• Cleft palate
• LIMITED MOUTH OPENING

Cardiovascular

• VSD

Neurological

• Dandy-Walker malformation
• hydrocephalus

Musculoskeletal

• Joint contractures

Considerations:

• DIFFICULT INTUBATION
• Positioning nightmare
• SBE prophylaxis

Links:

• Blackfan-Diamond Syndrome
• Dandy-Walker malformation